Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkBa/NF-kB pathway in limb girdle muscular dystrophy type 2A

S Baghdiguian; M Martin; I Richard; F Pons; C Astier; N Bourg; Ronald Thomas Hay; R Chemaly; G Halaby; J Loiselet; LV Anderson; A Lopez de Munain; M Fardeau; P Mangeat; JS Beckmann; G Lefranc

doi:10.1038/8385

Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkBa/NF-kB pathway in limb girdle muscular dystrophy type 2A

S Baghdiguian, M Martin, I Richard, F Pons, C Astier, N Bourg, Ronald Thomas Hay, R Chemaly, G Halaby, J Loiselet, LV Anderson, A Lopez de Munain, M Fardeau, P Mangeat, JS Beckmann, G Lefranc

School of Biology

Research output: Contribution to journal › Article › peer-review

256 Citations (Scopus)

Original language	English
Pages (from-to)	503-511
Number of pages	9
Journal	Nature Medicine
Volume	5
Issue number	5
DOIs	https://doi.org/10.1038/8385
Publication status	Published - May 1999

Keywords

MUSCLE-SPECIFIC CALPAIN
NUCLEAR-LOCALIZATION
DNA-FRAGMENTATION
EXPRESSION
PROTEIN
ACTIVATION
BCL-2
DOMAIN
VITRO
GENE

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Baghdiguian, S., Martin, M., Richard, I., Pons, F., Astier, C., Bourg, N., Hay, R. T., Chemaly, R., Halaby, G., Loiselet, J., Anderson, LV., Lopez de Munain, A., Fardeau, M., Mangeat, P., Beckmann, JS., & Lefranc, G. (1999). Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkBa/NF-kB pathway in limb girdle muscular dystrophy type 2A. Nature Medicine, 5(5), 503-511. https://doi.org/10.1038/8385

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title = "Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkBa/NF-kB pathway in limb girdle muscular dystrophy type 2A",

keywords = "MUSCLE-SPECIFIC CALPAIN, NUCLEAR-LOCALIZATION, DNA-FRAGMENTATION, EXPRESSION, PROTEIN, ACTIVATION, BCL-2, DOMAIN, VITRO, GENE",

author = "S Baghdiguian and M Martin and I Richard and F Pons and C Astier and N Bourg and Hay, {Ronald Thomas} and R Chemaly and G Halaby and J Loiselet and LV Anderson and {Lopez de Munain}, A and M Fardeau and P Mangeat and JS Beckmann and G Lefranc",

year = "1999",

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Baghdiguian, S, Martin, M, Richard, I, Pons, F, Astier, C, Bourg, N, Hay, RT, Chemaly, R, Halaby, G, Loiselet, J, Anderson, LV, Lopez de Munain, A, Fardeau, M, Mangeat, P, Beckmann, JS & Lefranc, G 1999, 'Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkBa/NF-kB pathway in limb girdle muscular dystrophy type 2A', Nature Medicine, vol. 5, no. 5, pp. 503-511. https://doi.org/10.1038/8385

TY - JOUR

T1 - Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkBa/NF-kB pathway in limb girdle muscular dystrophy type 2A

AU - Baghdiguian, S

AU - Martin, M

AU - Richard, I

AU - Pons, F

AU - Astier, C

AU - Bourg, N

AU - Hay, Ronald Thomas

AU - Chemaly, R

AU - Halaby, G

AU - Loiselet, J

AU - Anderson, LV

AU - Lopez de Munain, A

AU - Fardeau, M

AU - Mangeat, P

AU - Beckmann, JS

AU - Lefranc, G

PY - 1999/5

Y1 - 1999/5

KW - MUSCLE-SPECIFIC CALPAIN

KW - NUCLEAR-LOCALIZATION

KW - DNA-FRAGMENTATION

KW - EXPRESSION

KW - PROTEIN

KW - ACTIVATION

KW - BCL-2

KW - DOMAIN

KW - VITRO

KW - GENE

UR - http://www.scopus.com/inward/record.url?scp=0032941594&partnerID=8YFLogxK

U2 - 10.1038/8385

DO - 10.1038/8385

M3 - Article

SN - 1078-8956

VL - 5

SP - 503

EP - 511

JO - Nature Medicine

JF - Nature Medicine

IS - 5

ER -

Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IkBa/NF-kB pathway in limb girdle muscular dystrophy type 2A

Keywords

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